Melanocytic Neuroendocrine Tumour Of Infancy, A Rare Presentation Of Maxillary swelling.

Dr. Shrivastava Sunil; Dr Shah Pratik Vijay; Dr. Ravindra Kumar

Volume : VIII, Issue : VII, July - 2019

Melanocytic Neuroendocrine Tumour Of Infancy, A Rare Presentation Of Maxillary swelling.

Dr. Shrivastava Sunil, Dr Shah Pratik Vijay, Dr. Ravindra Kumar

Abstract :

Melanotic neuroectodermal tumour of infancy (MNTI) is rare, rapidly growing, pigmented neoplasm of neural crest origin. It is generally accepted as a benign tumour despite its rapid and locally destructive growth. It primarily affects the maxilla of infants during the first year of life. Surgical excision is considered as the treatment of choice. The recurrence rate varies between 10–15% and malignant behaviour has been reported in 6.5% of cases. We report a case of MNTI, associated with an erupted primary tooth in a 3 month old female child. We discuss the clinical, radiographic and histologic features of this rare tumour, as well as its surgical management and follow–up