IJSR International Journal of Scientific Research 2277 - 8179 Indian Society for Health and Advanced Research ijsr-9-4-24975 Original Research Paper TELANGIECTATIC OSTEOSARCOMA-AN IMAGING SPECTRUM Sridhar Dr. Uppin Shantiveer Dr. M. Phani Chakravarty Dr. April 2020 9 4 01 02 ABSTRACT

Context: Telengiectatic osteosarcomas (TOS) account for 2% to 12% of osteosarcomas. They have an osseous origin in the medulla of metaphysis of long bones; distal femur being most common site. In majority of tumor volume consists of large haemorrhagic or necrotic cavities accounting for 90% of lesion and small proportion of solid tissue. The walls, septae around haemorrhagic spaces are thick and nodular. Due to paucity of literature this study was undertaken. Aim: This study is aimed at delineating the imaging features of Talengiectatic osteosarcomas Methods and Material: All histopathologically proven cases of osteosarcoma attending our hospital were analysed. Six of the 35 cases were of TOS sub–type. Their imaging features– the bone–matrix consistency, zone of transition, fluid–fluid–level, periosteal reaction, soft–tissue and sclerosis were specifically studied. Results: All 6 were males and most were in age–group of 10–20 years. Three tumours were in femur and one each in humerus, tibia and radius. All were situated in metaphysis of long bones. Lesions were predominantly lytic with expansion of bone with cortical destruction soft tissue extension. There was periosteal reaction in the form of interrupted lamellar, sunburst, Codman’s triangle. 50% cases showed faint focal sclerosis at periphery. FFL were small and non–uniform with irregular walls and were observed in all cases. Conclusions: Telengiectatic osteosarcoma is a rare variety of Osteosarcomas. It has to be differentiated ABC. Lytic lesion, wide zone of transition and malignant periosteal reaction is usually observed in TOS. FFLs are usually small with irregular septae. Presence of sclerosis is diagnostic of TOS.