Globulomaxillary cyst is a notable, entrenched clinicopathologic element which has its alleged origin from entangled non–odontogenic epithelium. It was traditionally viewed as an incorporation or developmental cyst that emerged from entangled, non–odontogenic epithelium in the intersection of the globular part of the medial nasal process and the maxillary process. However, electron microscopic studies have invalidated the idea of fusion during the embryonic development of this area. Hence, the pathogenesis of globulomaxillary cyst is questioned. This article includes a case report of globulomaxillary cyst, its treatment and controversies related to it.