Mondini dysplasia is a type of congenital cochlear anomaly. It is described as incomplete partition type II with large vestibular aqueduct. We report two cases of a young females presenting with unilateral sensory neural hearing loss, diagnosed by imaging with HRCT temporal bone and MRI of inner ear as Mondini dysplasia before the occurrence of meningitis. This study briefly discusses Mondini dysplasia a subtype of cochlear anomalies, its imaging features and complications.