Acquired Dyke-Davidoff-Masson Syndrome presented with Crossed non-aphasia

Ritwik Ghosh; Arpan Mandal; Devlina Roy; Subrata Biswas

Volume : VIII, Issue : III, March - 2019

Acquired Dyke-Davidoff-Masson Syndrome presented with Crossed non-aphasia

Ritwik Ghosh, Arpan Mandal, Devlina Roy, Subrata Biswas

Abstract :

Dyke–Davidoff–Masson syndrome (DDMS) is a rare disease which is clinically characterized by hemiparesis, seizures, facial asymmetry, and intellectual disability. The classical radiological findings are cereal hemiatrophy, calvarial thickening, and hyperpneumatization of the frontal sinuses. This disease is a rare entity, commonly congenital and rarely acquired and it mainly presents in childhood. �Crossed non–aphasia�, a distinctly rare and interesting finding, is characterized by normal linguistic skills in a right–handed subject following damage to the left hemispheric linguistic cortex. However, these subjects show deficits in visuospatial skills, usually processed by the right hemisphere. In this report, we discuss a subject who presented with �crossed non–aphasia�, a clinical manifestation that often could go unnoticed, again in a rare case of DDMS with atypical radiological findings.