Neurofibromatosis Type 2 for Craniotomy: Anaesthesia Management of a Rare Case

Madhuri Dhabarde; Deepika Shukla; Jayshree Vaswani; Shubha Mohite

Volume : V, Issue : III, March - 2016

Neurofibromatosis Type 2 for Craniotomy: Anaesthesia Management of a Rare Case

Madhuri Dhabarde, Deepika Shukla, Jayshree Vaswani, Shubha Mohite

Abstract :

Introduction: Neurofiomatoses are autosomally dominant diseases having tendency to form tumours in ectodermal and mesodermal tissues. Neurofiomatosis type 2 (NF2) is rarer with birth incidence of 1:33,000–40,000. Case Description: We report the perioperative management of a 22 year old female, known case of NF2, presented with repeated episodes of projectile vomiting and decreased vision. MRI Brain showed bilateral vestibulo–cochlear schwannomas, left parafalcine and bilateral tentorial leaf meningiomas. Patient was posted for craniotomy and was managed successfully. Post operatively patient was shifted to ICU, electively ventilated overnight and extubated next day. After two days patient was shifted to ward and discharged on 10th day. Conclusion: NF2 is challenging to anaesthesiologists due to possibility of intracranial and intra–spinal canal tumours which is of relevance when patients are posted for other surgeries also. Multidisciplinary management with early diagnosis is mainstay of management.