Volume : VIII, Issue : V, May - 2019
SCHIZENCEPHALY:A CASE REPORT
Utpalendu Debnath
Abstract :
Schizencephaly, sometimes called agenetic porencephaly, is the term used to describe gray-matter lined clefts that extend through the entire cereal mantle, from the ependymal lining of the lateral ventricles to the pial covering of the cortex. A 1 year old male child was admitted with the history of delayed developmental milestone and spasticity of both upper and lower limbs since birth. The proper antenatal and natal history could not be obtained as the child was adopted. He was previously diagnosed as a case of cereal palsy. On physical examination, the child had microcephaly, no dysmorphism of face. Anterior fontanelle was normal. Sutures were normal and there was a global delay in the developmental milestones. Muscle tone of the upper and lower limbs showed spasticity with normal reflexes. Vitals signs were normal. Anthropometric measurements of weight and length were within normal limits. Plain CT scan of the ain showed wide CSF filled cleft in left frontal lobe and another narrow cleft in right parieto temporal lobe extending from cortex to lateral ventricles. The child was diagnosed as a case of bilateral schizencephaly. The incidence of schizencepaly is very low 1.5 in 1,000,000 live births. Only few cases have been described in the literature. The etiology of such phenomenon is also poorly understood.
Keywords :
Schizencephaly Cerebrospinal fluid Microcephaly Dysmorphism Anterior fontanelle Anthropometric measurement CT scan
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DOI : https://www.doi.org/10.36106/gjra
Cite This Article:
SCHIZENCEPHALY:A CASE REPORT, Utpalendu Debnath GLOBAL JOURNAL FOR RESEARCH ANALYSIS : Volume-8 | Issue-5 | May-2019
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SCHIZENCEPHALY:A CASE REPORT, Utpalendu Debnath GLOBAL JOURNAL FOR RESEARCH ANALYSIS : Volume-8 | Issue-5 | May-2019