QUALITY OF LIFE OF CHILDREN WITH HEMOPHILIA AS COMPARED TO THEIR HEALTHY SIBLINGS

Shanessa Budiarty; Selvi Nafianti; Sri Sofyani

Volume : IX, Issue : IV, April - 2020

QUALITY OF LIFE OF CHILDREN WITH HEMOPHILIA AS COMPARED TO THEIR HEALTHY SIBLINGS

Shanessa Budiarty, Selvi Nafianti, Sri Sofyani

Abstract :

Hemophilia is an X-linked recessive disorder caused by deficiency coagulation factor VIII or IX with bleeding manifestation. The impact of hemophilia on the quality of life (QoL) of hemophilic children and their healthy siblings is not well known. A cross-sectional study conducted among children with hemophilia and their healthy siblings aged 5 to 18 years old attended the Pediatric Hematology-Oncology outpatient clinic at Haji Adam Malik Hospital, Medan, from October to December 2019. The PedsQLTM 4.0 questionnaire was utilized to assess the QoL of the children. Children with hemophilia have lower QoL than their healthy siblings (p<0.001). However, adolescents had a lower QoL than the childhood hemophilia (p<0.001). Emotional, social and school functions were impaired QoL in the adolescent hemophilia.