Intravascular Papillary Endothelial Hyperplasia (Masson's Tumor)- A Rare Finding in the Orbital Region

Sant Prakash Kataria; Renuka Verma; Neha Yadav; Priya Jain; Gajender Singh; Rajeev Sen

Volume : VII, Issue : VIII, August - 2018

Intravascular Papillary Endothelial Hyperplasia (Masson's Tumor)- A Rare Finding in the Orbital Region

Sant Prakash Kataria, Renuka Verma, Neha Yadav, Priya Jain, Gajender Singh, Rajeev Sen

Abstract :

Intravascular papillary endothelial hyperplasia (IPEH) is a reactive proliferation of endothelial cells in the blood vessel. It typically present as a small, firm, painless lesion with red to blue discoloration.Most of the reported cases were usually located in the skin and subcutaneous tissue of the head and neck and extremities. Ocular involvement is very rare, and mostly involves the eyelids; whereas orbital lesions occur even less commonly.Here we report a rare case of IPEH in a 38 year old male who presented with solitary orbital mass in right eye with proptosis and diminished vision. Histopathological examination revealed papillary and tufted capillary endothelial hyperplasia with no atypia of endothelial lining. The hyperplastic endothelium showed immunohistochemical positivity for CD34 and vimentin. The diagnosis of IPEH (Masson�s tumor) was made.Prognosis of IPEH is excellent,if the lesion is completely excised. Although IPEH is benign, clinically this lesion is important because it present as a mass lesion or may be mistaken for angiosarcoma; it should be considered in the list of differentials of proptosis.