DIFFERENT ORTHODONTIC TREATMENT APPROACHES FOR CLEIDOCRANIAL DYSOSTOSIS - A REVIEW

DR HARSHIT PATEL; DR ANERI SHARMA; DR RAHUL BACHWANI; DR KHYATI MAHIDA; DR VAIBHAV CHAUDHARY; DR AAKASH HANDA

Volume : IX, Issue : IV, April - 2020

DIFFERENT ORTHODONTIC TREATMENT APPROACHES FOR CLEIDOCRANIAL DYSOSTOSIS - A REVIEW

Dr Harshit Patel, Dr Aneri Sharma, Dr Rahul Bachwani, Dr Khyati Mahida, Dr Vaibhav Chaudhary, Dr Aakash Handa

Abstract :

Cleidocranial dysostosis is a rare congenital skeletal disorder, associated with clavicular hypoplasia or aplasia, delayed closure of cranial fontanels, achycephalic skull, delayed exfoliation of primary dentition, eruption of permanent teeth, and multiple supernumerary and morphologic abnormalities of the maxilla and mandible. The disorder is caused by mutation in the CBFA1 gene, on the short arm of chromosome 6p21. The prevalence of cleidocranial dysostosis is estimated one per million, without sex or ethnic group predilection. The purpose of this paper is to describe the orthodontic treatment in a patient with cleidocranial dysostosis. Therapy may include removal of supernumerary teeth, surgical exposure of impacted teeth, and orthodontic treatment.