Anaesthetic management of a case of hereditary spherocytosis for splenectomy and open cholecystectomy

Dr. A.Rathna; Dr Haji Mohammed

Volume : V, Issue : XII, December - 2016

Anaesthetic management of a case of hereditary spherocytosis for splenectomy and open cholecystectomy

Dr. A. Rathna, Dr Haji Mohammed

Abstract :

Hereditary spherocytosis is a familial hemolytic disorder with an autosomal dominant transmission mainly although recessive inheritance is also seen. The heterogeneity of clinical features ranges from an asymptomatic condition to a fulminant haemolytic anaemia. It was first described in 1871 and is the most common cause of inherited haemolysis in Europe and North America within the Caucasian population, with an incidence of 1 in 5000 births. We report a case of a fifteen years old Indian male child with hereditary spherocytosis with anaemia, jaundice, splenomegaly and calculus cholecystitis who was posted for splenectomy and cholecystectomy.