ANAESTHETIC CONCERNS AND CHALLENGES IN A CASE OF APERTS SYNDROME AND ITS PERIOPERATIVE MANAGEMENT

Dr Sanjay K P; Dr Prasad Kulkarni; Dr Somasekharam P

Volume : IX, Issue : I, January - 2020

ANAESTHETIC CONCERNS AND CHALLENGES IN A CASE OF APERTS SYNDROME AND ITS PERIOPERATIVE MANAGEMENT

Dr Sanjay K P, Dr Prasad Kulkarni, Dr Somasekharam P

Abstract :

Apert syndrome is a congenital autosomal dominant disease characterized by craniosynostosis, achycephaly, midface hypoplasia , hypertelorism , choanal stenosis , multidigit hand and foot syndactyly. Anaesthetic implications include difficult airway, hyperactive airway disorder, difficult intravenous access, temperature dysregulation, repeat surgical procedures. Thorough pre - operative assessment of airway should be performed. Peri -operative management should include difficult airway cart preparation, temperature monitoring and watch for post-operative signs for airway obstruction. Regional anaesthesia may be difficult in these patients due to anatomic variations and therefore ultrasound guidance will be helpful. We report a case of 3-year-old girl of Aperts syndrome who presented to our institute for syndactyly release