A Case Report of Moyamoya Disease

Dr. Hiren Pandya; Dr. Prasanna Patel; Dr. Kanaiya Patel; Dr. Harsh Pathak

Volume : VIII, Issue : XI, November - 2019

A Case Report of Moyamoya Disease

Dr. Hiren Pandya, Dr. Prasanna Patel, Dr. Kanaiya Patel, Dr. Harsh Pathak

Abstract :

Moyamoya disease is a chronic, progressive occlusion of the circle of Willis arteries that leads to the development of characteristic collateral vessels seen on imaging, particularly cereal angiography. The disease may develop in children and adults, but the clinical features differ. Moyamoya disease occurs predominantly in Japanese individuals but has been found in all races with varying age distributions and clinical manifestations. As a result, moyamoya disease has been underrecognized as a cause of ischemic and hemorrhagic strokes. Moyamoya disease was first described in Japan by Takeuchi and Shimizu in 1957.[1] Although the disease is most common in Japan, many subsequent cases have been reported elsewhere, including North America and Europe.[2-3] Moyamoya disease is deemed a progressive steno-occlusive disease at terminal portions of the bilateral internal carotid arteries with the development of �moyamoya vessels� as collateral channels of circulation.[4] The appearance of these small, multiple vessels at the base of the ain on catheter angiography was originally described by the Japanese term moyamoya, which translates to �puff of smoke.�[5]