A case of Osler Weber Rendu syndrome and its anaesthetic implications

Vivek Chaudhary; Neha Rehalia; Monika; Ashish Minhas; Dheeraj Singha

Volume : IX, Issue : VIII, August - 2020

A case of Osler Weber Rendu syndrome and its anaesthetic implications

Vivek Chaudhary, Neha Rehalia, Monika, Ashish Minhas, Dheeraj Singha

Abstract :

Osler-Weber-Rendu disease or hereditary haemorrhagic telangiectasia (HHT) is an autosomal dominant genetic disorder. First recognised in the 19th century, this rare often undiagnosed familial disorder with abnormal vascular structures, causes bleeding from the nose and gastrointestinal tract. This condition is characterised by lack of communicating capillaries connecting arteries and veins resulting in multiple arteriovenous malformations (AVMs) and telangiectasia. We describe a case report of anaesthesia management of a patient with Osler-Weber-Rendu disease.